“ A Case Report on Best ’ s Vitelliform Macular Dystrophy . ”

Best’s disease also termed as vitelliform macular dystrophy is an autosomal dominant sorder which classically presents in childhood with the striking appearance of a yellow or orange yolk like lesion in the macula. Dr Franz Best, a German ophthalmologist, described the first pedigree in 1905. A 23year old male with complain of gradual reduction of vision distortion of images and presence of blind spots in the centre of his visual field in his both eyes from last 7 years presented to the out patient department with no similar family history. His visual acuity on snellen’s chart was found to be 6/24 B/E with improvement upto 6/18P in his right eye and no improvement in left eye on refraction. Fundus examination showed well circumscribed around 1.5 disc diameters in size yellowish lesion at fovea B/E with abnormal EOG, hyperfluorescent well circumscribed lesion at fovea on FFA and subretinal mound on OCT B/E all pointing towards the diagnosis of Best’s vitelliform macular dystrophy B/E.